Immunoglobulin A vasculitis

What is Immunoglobulin A vasculitis?

A rare, small-vessel vasculitis characterized by skin purpura, arthritis, abdominal and/or renal involvement, IgA tissue deposits (arterioles, capillaries, and venules) and circulating IgA immune complexes.

Other condition names

  • Anaphylactoid purpura
  • Henoch-Schönlein purpura
  • IgA vasculitis
  • Purpura rheumatica
  • Rheumatoid purpura

Inheritance type

Not applicable

Age of Onset

  • Childhood
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.