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X-linked retinoschisis

What is X-linked retinoschisis?

A rare disorder involving multiple structure of the eye characterized by reduced visual acuity in males due to juvenile macular degeneration. Clinical features such as vitreous hemorrhage, retinal detachment, and neovascular glaucoma can be observed in advanced stages.

Other condition names

  • X-linked juvenile retinoschisis
  • XLRS

Inheritance type

X-linked recessive

Prevalence

  • Worldwide: 1-9 in 100,000
  • Europe: 1-9 in 100,000

Age of Onset

  • Adolescent
  • Adult
  • Childhood
  • Infancy
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.