Acanthosis nigricans-insulin resistance-muscle cramps-acral enlargement syndrome

What is Acanthosis nigricans-insulin resistance-muscle cramps-acral enlargement syndrome?

This syndrome is characterised by the association of acanthosis nigricans, insulin resistance, severe muscle cramps and acral hypertrophy.

Prevalence

  • Worldwide: <1 in 1,000 000

Age of Onset

  • Adult
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.