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Behçet disease
What is Behçet disease?
A rare, chronic, relapsing, multisystemic vasculitis characterized by mucocutaneous lesions, as well as articular, vascular, ocular and central nervous system manifestations.
Inheritance type
Multigenic/multifactorial
Prevalence
United States: 1-9 in 100,000
Age of Onset
Adolescent
Adult
Childhood
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.