Congenital lobar emphysema

What is Congenital lobar emphysema?

A respiratory abnormality characterized by respiratory distress due to hyperinflation of one or more affected lobes of the lung.

Other condition names

  • Congenital lobar hyperinflation
  • Infantile lobar hyperinflation

Inheritance type

Not applicable


  • Worldwide: 1-9 in 100,000

Age of Onset

  • Adult
  • Childhood
  • Infancy
  • Neonatal
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