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Nephrogenic diabetes insipidus

What is Nephrogenic diabetes insipidus?

A rare, genetic renal tubular disease that is characterized by polyuria with polydipsia, recurrent bouts of fever, constipation, and acute hypernatremic dehydration after birth that may cause neurological sequelae.

Inheritance type

Autosomal dominant, Autosomal recessive, X-linked recessive

Prevalence

  • Europe: 1-9 in 1,000 000

Age of Onset

  • Infancy
  • Neonatal
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.